von Hippel-Lindau disease (vHL)

Case contributed by Dr Hani Makky Al Salam

Presentation

Known von Hippel-Lindau disease. Left nephrectomy for renal cell carcinoma.

Patient Data

Age: 30 years
Gender: Male

Multiple right renal cysts are seen, with at least two lesions showing early enhancement during arterial phase, and rapid-washout during delayed phase, suggesting possible small renal cell carcinomas.

Pancreatic cysts, another characteristic feature of von Hippel-Lindau syndrome are also seen.

Case Discussion

von Hippel-Lindau syndrome with renal cell carcinoma, renal cysts and pancreatic cysts.

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