Presentation
History of tumor resection at the posterior fossa
Patient Data
Multiple enhancing intra-axial lesions in the posterior fossa. Cystic lesion with no mural nodule also detected in the right cerebellum.
Cystic mass with a mural nodule was detected in the conus medullaris. The mural nodule showed vivid enhancement on post-contrast images. Some small multiple enhancing lesions which are similar to those in the brain were also identified in this area.
A homogenous,well-circumscribe mass at the pancreatic head was observed. The mass vividly enhanced on post-contrast images. No fat infiltration or regional lymphadenopathy was found.
Case Discussion
The pathological result of the posterior fossa tumor was hemangioblastoma.
The pancreatic mass was surgically removed and pathologically proven endocrine tumor.
Regarding the pathological result of the pancreatic and posterior fossa masses, the imaging features on MRI of the brain and spine are characteristic of Von Hippel-Lindau syndrome.
Besides CSN and pancreatic manifestations, Von Hippel-Lindau syndrome is characterized by tumors in other organs such as renal cell carcinomas, retinal hemangioblastomas, or liver cysts.