Presentation
Pelvic cystic lesion on ultrasound.
Patient Data
The right kidney is not visualized (agenesis) with agenesis of the right renal vessels and normal right adrenal gland.
Right-sided tortuously cystic dilated seminal vesicle with a rudimentary ureter connected to it.
The left seminal vesicle is mildly dilated, measuring 19 mm in diameter, suggesting secondary ejaculatory duct obstruction.
Case Discussion
Zinner syndrome is a triad of mesonephric (Wolffian) duct anomalies comprising unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ejaculatory duct obstruction.
There is an association between congenital malformations of the seminal vesicle and the ipsilateral upper urinary tract because both the ureteral buds and the seminal vesicles originate from the mesonephric (Wolffian) duct.
Zinner syndrome is also considered the male counterpart of Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome in females.
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