What is the main cause of mortality in the neonatal period?
Pulmonary hypoplasia due to oligohydramnios.
What hepatobiliary abnormalities are associated with this condition?
Congenital hepatic fibrosis, Caroli disease
The ultrasound performed shortly after birth shows essentially the same features as the antenatal ultrasound, with enlarged echogenic kidneys, without corticomedullary differentiation. No hepatic or biliary tree abnormality identified (not shown).