Pericardial agenesis

Discussion:

Pericardial agenesis (partial) is a rare cardiac defect. Radiologically, it presents with the following :

  • levoposition of the heart
  • prominent pulmonary artery
  • air interface in the aorto-pulmonary window or between the base of the heart and the diapgragm
CT-scan is better than MRI for this diagnosis, since it has more spatial resolution. The pericardial defect will be seen. A complete pericardial defect is a benign condition, while patients with partial agenesis may have cardiac herniation through the defect. They should be managed surgically.
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