Retinoblastoma is the commonest ocular malignancy in childhood, occuring chiefly in those under 4 years of age. This is a case of a retinoblatoma with intraorbital and intracranial extension along the optic nerve and optic chiasma with a contiguous suprasellar mass and resultant hydrocephalus in keeping with stage IV disease.
Stage IV: metastatic disease
- A: haematogeneous metastasis without CNS involvement
- single lesion
- multiple lesions or
OR
- B: CNS metastatic involvement
- pre-chiasmatic lesion
- CNS mass
- leptomeningeal disease