Cranial nerve lesions present in virtually all patients with neurofibromatosis type 2 (NF2). They are often multiple, with vestibular schwannomas (VS) being the most common NF2-related schwannomas. The finding of bilateral VS is almost pathognomonic of NF2 by imaging. Nonvestibular schwannomas also occur in around 50% of cases (such as trigeminal, oculomotor). The associated imaging features of NF2 are meningiomas (50%), cord ependymomas (often multiple) and schwannomas of spinal nerve roots.