What is the prognosis for this fetus? What about the lungs?
75% have death within 24 hours of delivery, pulmonary hypoplasia occurs secondary to the severe oligohydramnios.
In the perinatal form of ARPKD, like in this case, what is the likelihood of hepatic fibrosis?
Minimal hepatic fibrosis is seen in the perinatal type of ARPKD. The infantile and juvenile types tend to show moderate and gross hepatic fibrosis, respectively.
Severe oligohydramnios and an enlarged abdomen circumference caused by enlarged kidneys.
Both kidneys were partially replaced by numerous irregular cystic structures (1-3mm) with echogenic tissue separating them.