What is the diagnosis?
Lhermitte-Duclos disease (LDD) (also known as dysplastic cerebellar gangliocytoma).
What is the WHO grade of this lesion?
WHO grade I
What syndromic association does it have?
Cowden syndrome (multiple hamartoma syndrome) - when present it is then termed Lhermitte-Duclos-Cowden syndrome.
MRI confirms the abnormality. The mass is striated and hyperintense on T2 and grey matter isointense on T1, with no restricted diffusion and no contrast enhancement.