Cystic fibrosis


The patient died due to severe respiratory failure

Chest x-rays are insensitive to the early changes of cystic fibrosis, with changes seen on HRCT in 65% of patients with CF and normal CXR1.  Later changes on x-rays include:

  • bronchiectasis;
  • hyperinflation;
  • lobar collapse;
  • pulmonary arterial enlargement due to pulmonary arterial hypertension is seen in patients with long standing disease;