Scimitar syndrome

Discussion:

This patient was subsequently referred externally for CTA which confirmed an anomalous right lower pulmonary vein draining into the IVC, in keeping with PAPVR.

Scimitar syndrome represents a combination of pulmonary hypoplasia and partial anomalous pulmonary venous return (PAPVR).

It almost exclusively occurs on the right side and the anomalous pulmonary vein can drain into the:

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