MRI features of diastematomyelia, also known as a split cord malformation type I which is the classic type characterized by:

• duplicated dural sac with midline spur (osseous or osteocartilaginous)
• associated hydromyelia is common
• vertebral abnormalities such as hemivertebrae, butterfly vertebrae, spina bifida
• cutaneous pigmentation, hypertrichosis, hemangioma are common
• patients are usually symptomatic presenting with scoliosis and tethered cord syndrome