Craniofacial fibrous dysplasia

Discussion:

Craniofacial fibrous dysplasia is a benign developmental tumor-like bone lesion. It is one of four types of fibrous dysplasia and is characterized by involvement of the skull and facial bones. 

It is a chronic, slowly progressive process that produces craniofacial deformities and complications that usually arise from compression upon skull foramina and their neurovascular contents, and other intracranial structures. The most common manifestations are neurological symptoms such as hearing loss, visual loss, headache, and proptosis.

The suggestive features are the facial deformity, bony expansion with a heterogeneous appearance of hypointensity at T2WI that is due to the fibro-osseous ground-glass matrix. It typically shows heterogeneous contrast enhancement.

See case (rID-64500) for spinal and rib lesions in this patient.

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