Sphenoid wing dysplasia (bare orbit)


Dysplastic and defective right greater wing of sphenoid bone; consistent with right bare orbit; suggesting the possibility of neurofibromatosis type I (NFI). Clinical examination of this child revealed skin nodules and cafe au lait patches as well as axillary freckling. The previous ileo-colic intussusception might have been related to neurofibromatosis of the ileum.