CT
The distal aortic arch is dilated with an aneurysmal origin of the retro-esophageal aberrant right subclavian artery (Kommerell diverticulum).
There are thoracic and abdominal anatomic variants and anomalies:
- atrial situs, atrioventricular and ventriculoarterial connections are normal; one may discuss two atria with left morphology. No abnormal pulmonary venous return. There is absence of the hepatic segment of the IVC with azygos continuation. No persistent left SVC.
- the bilateral mainstem bronchi show left morphology and each lungs have two lobes and one fissure (bilateral bilobed lungs)
- liver and gallbladder are essentially median in position
- polysplenia
- the stomach is on the right, small bowel loops all located on the left, large bowel is located on the right: findings suggestive of a mirrored intestinal nonrotation
- mesenteric vessels are reversed
There is a pouch-like structure located below the level of the aortic valve annulus, consistent with a membranous diverticulum of the interventricular septum, while the sinus of Valsalva and aortic valve cusps are grossly normal.
This case is a joint interpretation of imaging with Dr P. Mascarel, who is the prime reporter.