Isolated absence of the right pulmonary artery


Additional information garnered from patient's file reinforces diagnosis of IUAPA:

  • hypoplastic right lung with severely decreased ventilation and no perfusion, discovered incidentally on a V/Q scan performed at toddlerhood due to suspicion of foreign body aspiration
  • findings at report for chest CT performed at age 5 very similar to above exam
  • transthoracic echocardiography at age 8 demonstrated no cardiac anomaly
  • patient's mother mentions mediastinal shift to right on chest x-ray taken at age 4 months

    Differential diagnosis of a small lung on plain film includes: