Complete pancreatic lipomatosis: cystic fibrosis

Discussion:

There are a number of causes of complete pancreatic lipomatosis:

  • cystic fibrosis (most common cause in childhood)  
  • metabolic/endocrine: hyperlipidemia, diabetes mellitus
  • storage disease: hemochromatosis
  • drugs: steroids
  • infectious: viral infection, sepsis
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