Primary pulmonary disease where diffuse cysts are the predominate feature:
- pulmonary Langerhans cell histiocytosis: can be irregular in outline
- lymphocytic interstitial pneumonitis (LIP)
- lymphangioleiomyomatosis 3 with or without tuberous sclerosis
- tracheobronchial papillomatosis
- Sjogren syndrome
- neurofibromatosis 1
- Birt-Hogg-Dubé syndrome (rare) 4
- pulmonary mesenchymal cystic hamartoma (rare) 2
- as a pulmonary manifestation of light chain deposition disease 8
Acquired cystic lung disease or cysts as a secondary feature of a primary disease:
- honeycombing in UIP pattern 5
- cystic bronchiectasis
- pulmonary laceration in trauma
- pneumocystis pneumonia
- sarcoidosis