Constellation of malrotation, polysplenism, and left IVC supports the diagnosis of _______________
Heterotaxy syndrome - specifically left isomerism.
How many pulmonary fissures would you expect a patient with left isomerism to have?
Bilateral bilobed lungs. Patients with right isomerism have trilobed lungs.
- Free gas is present, predominately within the right upper abdomen. A site of perforation is not evident. Mild bowel wall thickening involves jejunal loops without significant surrounding inflammatory change.
- Malrotation. Jejunal loops are located within the right upper quadrant. The caecum is left-sided. The duodenum can be traced with D3 extending anteriorly and to the right from the inferior duodenal flexure.
- The portal vein passes anterior to the neck of the pancreas.
- Polysplenism.
- Left-sided IVC.