Items tagged “cases3”

344 results found
Article

Ileostomy

An ileostomy is a surgical method in which a loop of the distal small bowel is connected and opened through the outer abdominal wall to artificially create a connection and bypass the large bowel. Pathology Types There are two types of ileostomies: permanent end ileostomy A permanent end il...
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Infantile fibrosarcoma

Infantile fibrosarcomas also known as congenital fibrosarcoma, infantile fibrosarcoma-like tumor, and cellular congenital mesoblastic nephroma are locally aggressive rarely metastasizing fibroblastic tumors found in the pediatric population. Epidemiology Infantile fibrosarcomas are most common...
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Low-grade myofibroblastic sarcoma

Low-grade myofibroblastic sarcomas, also known as myofibrosarcoma are locally aggressive rarely metastasizing fibroblastic tumors. Epidemiology Low-grade myofibroblastic sarcomas most commonly occur in adults in the 4th and 5th decade of life with a minor male predominance and are rarely found...
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Juvenile hyaline fibromatosis

Juvenile hyaline fibromatosis, also known as hyaline fibromatosis syndrome or infantile systemic hyalinosis is a rare autosomal recessive syndrome outlined by painful, abnormal, often deforming deposits of hyalinized fibrous material in the extracellular matrix of the skin, subcutaneous soft tis...
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Inclusion body fibromatosis

Inclusion body fibromatosis is a superficial benign myofibroblastic tumor characterized by eosinophilic intracytoplasmatic inclusions. These tumors are also known under the terms infantile digital fibroma or fibromatosis, recurring digital fibroma of childhood, recurring digital fibrous tumor of...
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Angiomyofibroblastoma

Angiomyofibroblastomas are benign mesenchymal neoplasms usually found in the pelvis or perineum, especially the vulva. Epidemiology Angiomyofibroblastomas are uncommon tumors predominantly found in adult women usually between menarche and menopause. Approximately 10% of these tumors have been ...
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Nuchal type fibroma

Nuchal-type fibromas or nuchal fibromas are rare benign fibrous tumors arising from the connective tissues of the neck. Terminology The term 'collagenosis nuchae' is now discouraged 1. Epidemiology Nuchal-type fibromas are rare tumors and are mainly found in men in their 30s and 40s 1. Asso...
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Acral fibromyxoma

Acral fibromyxomas, also known as superficial acral fibromyxomas or digital fibromyxomas are benign mesenchymal proliferations prone to recurrence usually found in the subungual and periungual sites of the digits. Terminology The term 'cellular digital fibroma' is not recommended 1,2. Epidemi...
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Plexiform fibrohistiocytic tumor

Plexiform fibrohistiocytic tumors (PFHT) are dermal or subcutaneous soft tissue neoplasms of uncertain behavior with biphasic tumor morphology and a plexiform growth pattern.  Epidemiology Plexiform fibrohistiocytic tumors are rare tumors. They can occur over a wide age range but are usually s...
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Giant cell tumor of soft tissue

Giant cell tumors of soft tissue are fibrohistiocytic neoplasms of uncertain behavior that show morphological similarities to giant cell tumors of bone but are not related genetically. Terminology Giant cell tumor of low malignant potential is a term that should not be used any longer 1. Epid...
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Composite hemangioendothelioma

Composite hemangioendotheliomas are locally aggressive and rarely metastasizing vascular tumors consisting of different and histologically distinct elements. Epidemiology Composite hemangioendotheliomas are very rare and mostly seen in adults. Women are slightly more commonly affected 1,2. Di...
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Pseudomyogenic hemangioendothelioma

Pseudomyogenic hemangioendotheliomas, also known as epithelioid sarcoma-like hemangioendotheliomas, are locally aggressive and rarely metastasizing vascular neoplasms with histological similarities to myoid tumors and epithelioid sarcomas.  Epidemiology Pseudomyogenic hemangioendotheliomas are...
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IgG4-related arteritis and periarteritis

IgG4-related arteritis and periarteritis is a form of IgG4-related cardiovascular disease, in which multi-vessel involvement is very common. Epidemiology IgG4-related arteritis and periarteritis predominantly affect men above 60 years of age 1. Associations Conditions associated with IgG4-re...
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Hypoplastic circumflex artery

A hypoplastic circumflex artery refers to a small-sized circumflex artery (Cx) with a small lumen and a short course. Epidemiology Hypoplastic circumflex arteries are rarely described in the literature. Associations Clinical conditions associated with a hypoplastic circumflex artery include ...
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Congenital coronary ostial stenosis or atresia

Congenital coronary ostial stenosis and coronary atresia are intrinsic congenital coronary artery anomalies in which there is either an intrinsic narrowing or an absent coronary ostium. Epidemiology Coronary ostial stenosis and atresia are reportedly extremely rare conditions 1,2. Association...
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Segmental anatomy of the coronary arteries

The segmental anatomy of the coronary arteries has been originally developed and published by the Council on Cardiovascular Surgery and the American Heart Association (AHA). It is widely used for the description of coronary findings in particular within the scope of coronary artery disease. Cor...
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Congenital absence of the circumflex artery

Congenital absence of the circumflex artery describes the lack of development of the circumflex artery within the atrioventricular groove. Epidemiology Congenital absence of the circumflex artery is a very rare coronary artery anomaly. Associations Congenital absence of the circumflex artery...
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Catel-Manzke syndrome

Catel-Manzke syndrome is a digitopalatal syndrome initially described in 1961. Inheritance pattern is unknown. Radiographic findings include micronagthia and accessory ossicles at the bases of the metacarpals.
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Atrioventricular nodal artery

The atrioventricular (AV) nodal artery is a small artery supplying the atrioventricular septal area and the atrioventricular node. Gross anatomy The atrioventricular nodal artery usually courses through the inferior pyramidal space of the heart. Origin The origin of the atrioventricular noda...
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Inferior pyramidal space of the heart

The inferior pyramidal space of the heart is an area filled with epicardial adipose tissue at the backside or diaphragmatic side of the heart immediately beneath the crux cordis. Gross anatomy The inferior pyramidal space is a pyramid-shaped fibrofatty structure between the two septal atrial w...