Items tagged “cases3”
343 results found
Article
Infantile fibrosarcoma
Infantile fibrosarcomas also known as congenital fibrosarcoma, infantile fibrosarcoma-like tumor, and cellular congenital mesoblastic nephroma are locally aggressive rarely metastasizing fibroblastic tumors found in the pediatric population.
Epidemiology
Infantile fibrosarcomas are most common...
Article
Low-grade myofibroblastic sarcoma
Low-grade myofibroblastic sarcomas, also known as myofibrosarcoma are locally aggressive rarely metastasizing fibroblastic tumors.
Epidemiology
Low-grade myofibroblastic sarcomas most commonly occur in adults in the 4th and 5th decade of life with a minor male predominance and are rarely found...
Article
Juvenile hyaline fibromatosis
Juvenile hyaline fibromatosis, also known as hyaline fibromatosis syndrome or infantile systemic hyalinosis is a rare autosomal recessive syndrome outlined by painful, abnormal, often deforming deposits of hyalinized fibrous material in the extracellular matrix of the skin, subcutaneous soft tis...
Article
Inclusion body fibromatosis
Inclusion body fibromatosis is a superficial benign myofibroblastic tumor characterized by eosinophilic intracytoplasmatic inclusions. These tumors are also known under the terms infantile digital fibroma or fibromatosis, recurring digital fibroma of childhood, recurring digital fibrous tumor of...
Article
Angiomyofibroblastoma
Angiomyofibroblastomas are benign mesenchymal neoplasms usually found in the pelvis or perineum, especially the vulva.
Epidemiology
Angiomyofibroblastomas are uncommon tumors predominantly found in adult women usually between menarche and menopause. Approximately 10% of these tumors have been ...
Article
Nuchal type fibroma
Nuchal-type fibromas or nuchal fibromas are rare benign fibrous tumors arising from the connective tissues of the neck.
Terminology
The term 'collagenosis nuchae' is now discouraged 1.
Epidemiology
Nuchal-type fibromas are rare tumors and are mainly found in men in their 30s and 40s 1.
Asso...
Article
Acral fibromyxoma
Acral fibromyxomas, also known as superficial acral fibromyxomas or digital fibromyxomas are benign mesenchymal proliferations prone to recurrence usually found in the subungual and periungual sites of the digits.
Terminology
The term 'cellular digital fibroma' is not recommended 1,2.
Epidemi...
Article
Plexiform fibrohistiocytic tumor
Plexiform fibrohistiocytic tumors (PFHT) are dermal or subcutaneous soft tissue neoplasms of uncertain behavior with biphasic tumor morphology and a plexiform growth pattern.
Epidemiology
Plexiform fibrohistiocytic tumors are rare tumors. They can occur over a wide age range but are usually s...
Article
Giant cell tumor of soft tissue
Giant cell tumors of soft tissue are fibrohistiocytic neoplasms of uncertain behavior that show morphological similarities to giant cell tumors of bone but are not related genetically.
Terminology
Giant cell tumor of low malignant potential is a term that should not be used any longer 1.
Epid...
Article
Composite hemangioendothelioma
Composite hemangioendotheliomas are locally aggressive and rarely metastasizing vascular tumors consisting of different and histologically distinct elements.
Epidemiology
Composite hemangioendotheliomas are very rare and mostly seen in adults. Women are slightly more commonly affected 1,2.
Di...
Article
Pseudomyogenic hemangioendothelioma
Pseudomyogenic hemangioendotheliomas, also known as epithelioid sarcoma-like hemangioendotheliomas, are locally aggressive and rarely metastasizing vascular neoplasms with histological similarities to myoid tumors and epithelioid sarcomas.
Epidemiology
Pseudomyogenic hemangioendotheliomas are...
Article
IgG4-related arteritis and periarteritis
IgG4-related arteritis and periarteritis is a form of IgG4-related cardiovascular disease, in which multi-vessel involvement is very common.
Epidemiology
IgG4-related arteritis and periarteritis predominantly affect men above 60 years of age 1.
Associations
Conditions associated with IgG4-re...
Article
Hypoplastic circumflex artery
A hypoplastic circumflex artery refers to a small-sized circumflex artery (Cx) with a small lumen and a short course.
Epidemiology
Hypoplastic circumflex arteries are rarely described in the literature.
Associations
Clinical conditions associated with a hypoplastic circumflex artery include ...
Article
Congenital coronary ostial stenosis or atresia
Congenital coronary ostial stenosis and coronary atresia are intrinsic congenital coronary artery anomalies in which there is either an intrinsic narrowing or an absent coronary ostium.
Epidemiology
Coronary ostial stenosis and atresia are reportedly extremely rare conditions 1,2.
Association...
Article
Segmental anatomy of the coronary arteries
The segmental anatomy of the coronary arteries has been originally developed and published by the Council on Cardiovascular Surgery and the American Heart Association (AHA). It is widely used for the description of coronary findings in particular within the scope of coronary artery disease.
Cor...
Article
Congenital absence of the circumflex artery
Congenital absence of the circumflex artery describes the lack of development of the circumflex artery within the atrioventricular groove.
Epidemiology
Congenital absence of the circumflex artery is a very rare coronary artery anomaly.
Associations
Congenital absence of the circumflex artery...
Article
Catel-Manzke syndrome
Catel-Manzke syndrome is a digitopalatal syndrome initially described in 1961. Inheritance pattern is unknown. Radiographic findings include micronagthia and accessory ossicles at the bases of the metacarpals.
Article
Atrioventricular nodal artery
The atrioventricular (AV) nodal artery is a small artery supplying the atrioventricular septal area and the atrioventricular node.
Gross anatomy
The atrioventricular nodal artery usually courses through the inferior pyramidal space of the heart.
Origin
The origin of the atrioventricular noda...
Article
Inferior pyramidal space of the heart
The inferior pyramidal space of the heart is an area filled with epicardial adipose tissue at the backside or diaphragmatic side of the heart immediately beneath the crux cordis.
Gross anatomy
The inferior pyramidal space is a pyramid-shaped fibrofatty structure between the two septal atrial w...
Article
Triangle of Koch
The triangle of Koch or Koch’s triangle is an important landmark for atrioventricular catheter ablation procedures for the localization of the atrioventricular node.
Gross anatomy
From a right atrial viewpoint, the triangle of Koch is delineated by the hinge of the septal tricuspid valve leafl...