Items tagged “congenital heart disease”
25 results found
Article
Ventricular septal defect
Ventricular septal defects (VSD) represent a hole or pathway in the interventricular septum that allows for communication between the right and left ventricles. It typically results in a left-to-right shunt.
Epidemiology
They represent one of the most common congenital cardiac anomalies and ma...
Article
Tetralogy of Fallot
Tetralogy of Fallot (TOF) is the most common cyanotic congenital heart condition with many cases presenting after the newborn period. It has been classically characterized by the combination of ventricular septal defect (VSD), right ventricular outflow tract obstruction (RVOTO), overriding aorta...
Article
Ebstein anomaly
Ebstein anomaly is an uncommon congenital cardiac anomaly, characterized by a variable developmental anomaly of the tricuspid valve.
Epidemiology
The anomaly accounts for only ~0.5% of congenital cardiac defects 6,7, although it is the most common cause of congenital tricuspid regurgitation. T...
Article
Total anomalous pulmonary venous return
Total anomalous pulmonary venous return (TAPVR) is a cyanotic congenital heart anomaly with abnormal drainage anatomy of the entire pulmonary venous system. This contrasts with partial anomalous pulmonary venous return (PAPVR) where only part of the pulmonary venous anatomy is abnormal.
In TAPV...
Article
Arrhythmogenic right ventricular cardiomyopathy
Arrhythmogenic right ventricular cardiomyopathy (ARVC), also referred to as arrhythmogenic right ventricular dysplasia (ARVD) or simply arrhythmogenic cardiomyopathy, is a cardiomyopathy that is one of the more common causes of sudden cardiac death in young patients.
Epidemiology
The estimate...
Article
Uhl anomaly
Uhl anomaly is an unusual cardiac disorder which affects the right ventricle where there is an almost complete absence of right ventricular myocardium, normal tricuspid valve, and preserved septal and left ventricular myocardium.
Clinical presentation
Presentation usually occurs in the neonata...
Case
Infracardiac total anomalous pulmonary venous return
Published
15 Nov 2013
97% complete
X-ray
Case
Arterial switch procedure
Published
26 Oct 2014
86% complete
CT
Annotated image
Case
Congenital pulmonary valve stenosis
Published
07 Mar 2015
95% complete
X-ray
MRI
Article
Cardiovascular shunts
Cardiovascular (cardiac) shunts are abnormal connections between the pulmonary and systemic circulations. Most commonly they are the result of congenital heart disease.
Pathology
Blood can either be shunted from the systemic circulation to pulmonary circulation (i.e. 'left-to-right shunt') or ...
Article
Surgically-created cardiac shunts (mnemonic)
A mnemonic for surgically-created cardiac shunts for congenital heart disease is:
Great Flow Really Would Be Perfect
The mnemonic is ordered by the position of the shunt antegrade to normal blood flow through the heart, proceeding from the systemic venous system into the right heart, and then...
Case
Horseshoe lung
Published
01 Jul 2015
86% complete
CT
Case
D-TGA, atrial switch procedure and pacemaker
Published
14 Sep 2015
93% complete
CT
X-ray
Case
Truncus arteriosus
Published
06 Nov 2015
83% complete
CT
Case
Fontan procedure
Published
13 Nov 2015
77% complete
CT
Case
Pulmonary atresia with intact interventricular septum
Published
04 Feb 2016
75% complete
X-ray
Case
Truncus arteriosus - Van Praagh type A3
Published
22 Aug 2016
98% complete
CT
Article
Aorto-ventricular tunnel
Aorto-ventricular tunnel (AVT) is an extremely rare form of congenital heart disease, representing an anomalous extracardiac communication between the ascending aorta and the left or right ventricles.
Terminology
In most cases the anomalous communication is between the aorta and the left ventr...
Case
d-TGA with atrial switch
Published
23 Feb 2020
95% complete
MRI
Article
Double inlet left ventricle
Double inlet left ventricle (DILV) describes a congenital cardiac anomaly in which both atrioventricular valves are associated with a single ventricle which demonstrates left ventricular morphology.
Epidemiology
This uncommon entity constituents 1% of all congenital cardiac anomalies, and is o...