Items tagged “soft tissue tumours”
6 results found
Article
WHO classification of tumors of soft tissue
The World Health Organization (WHO) classification of soft tissue tumors is the most widely used pathology-based classification system for such disorders. The current revision, part of the 5th edition of the WHO classification of soft tissue and bone tumors (volume 3), was published in 2020 and ...
Article
Hybrid nerve sheath tumor
Hybrid nerve sheath tumors or hybrid peripheral nerve sheath tumors (HPNST) are benign peripheral nerve sheath tumors displaying combined morphological characteristics of more than one of the conventional tumor types such as schwannoma neurofibroma or perineurioma. Recognized combinations are:
...
Article
Composite hemangioendothelioma
Composite hemangioendotheliomas are locally aggressive and rarely metastasizing vascular tumors consisting of different and histologically distinct elements.
Epidemiology
Composite hemangioendotheliomas are very rare and mostly seen in adults. Women are slightly more commonly affected 1,2.
Di...
Article
Ectomesenchymoma
Ectomesenchymomas are biphasic or composite malignant soft tissue tumors with rhabdomyosarcoma resembling parts and neuronal or neuroblastic features.
Terminology
The term ‘gangliorhabdomyosarcoma’ is no longer recommended.
Epidemiology
Ectomesenchymomas are very rare and usually occur in in...
Article
Giant cell fibroblastoma
Giant cell fibroblastomas are locally aggressive mesenchymal neoplasms closely related to dermatofibrosarcoma protuberans.
Epidemiology
Giant cell fibroblastomas are rare. They are usually but not exclusively found in children within the first decade of life, adult cases are rare. Boys are mor...
Article
Inflammatory leiomyosarcoma
Inflammatory leiomyosarcomas are malignant tumors with smooth muscle differentiation and a prominent inflammatory infiltrate that were just recently recognized as a distinct entity by the WHO in 2020 1-3.
Epidemiology
Inflammatory leiomyosarcomas are very rare lesions with most cases seen in a...
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