The case shows the cervical cord split into two hemicords (diastematomyelia) with multilevel vertebral fusion (Klippel-Feil syndrome).

Cervical diastematomyelia/split cord malformation is a rare congenital abnormality.

Diastematomyelia is a congenital abnormality in which the spinal cord is longitudinally divided. It commonly occurs in the thoracic or lumbar regions. It rarely occurs in the cervical spine.

Diastematomyelia is often found in association with other congenital abnormalities, in conjunction with the Klippel-Feil syndrome and Chiari type II malformations.

Diastematomyelia could be either a true duplication of the spinal cord, with each cord surrounded by separate dural sheaths or a partial separation of the cord, with or without septum.

This case is courtesy of Dr. Marwa Romaih, MD of Radiodiagnosis.