Biliary atresia is a congenital anomaly in which there is a variable degree of atresia of the extrahepatic biliary ducts. with an incidence of approximately 1:15000 having male prediction.

A baby with congenital atresia is normal at birth, with symptoms starting to develop after 2 weeks to 2 months of age. Less than 10% of cases present with syndromic conditions such as polysplenia, interrupted IVC, etc.

In this case, the gall bladder is hypoplastic with a length of less than 19 mm, with non-visualisation of the common hepatic duct and common bile duct, and increased periportal signal intensity along with hepatomegaly. Overall features are consistent with biliary atresia Kasai type 3.