Electrocardiogram without significant changes. Chest radiography showed cardiomegaly. An echocardiogram showed dissection of the ascending aorta with significant aortic valve insufficiency and ventricular dysfunction.

The patient presented two siblings with the diagnosis of Marfan syndrome manifesting as right lens dislocation, dolichocephaly and joint hypermobility.

After CT angiography, the patient underwent implantation of a biological tube by the Bentall technique, with reimplantation of the coronary ostia.

Hospital discharge after 3 days, hemodynamically stable.