Lymphocytic interstitial pneumonia in Sjögren syndrome

Discussion:

Lymphocytic interstitial pneumonia in Sjögren syndrome is characterized by lymphocytic infiltration of the small airway or alveolar septa resulting in CT apperance of centrilobular nodules and peribronchiolar ground glass opacities which eventually evolve to form thin walled cysts measuring 5-30 mm. Presence of cysts are useful in differentiating lymphocytic interstitial pneumonia from lymphoma which demonstrate consolidation, larger nodules, or associated pleural effusion.

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