Nasal chondromesenchymal hamartoma (NCMH) is a rare, pediatric benign tumor that most commonly affects children under one year of age ^1-3. Patients often present with symptoms based on tumor location and compression on adjacent structures. Recurrence after surgery is common in incomplete resections due to its infiltrative nature. In addition, there is a documented association between NCMH and the DICER1 familial tumor susceptibility syndrome. This syndrome increases the risk of other tumors including Sertoli-Leydig tumors, granulosa cell tumor, gynandroblastoma, ovarian sex cord-stromal tumor, cystic nephroma, pleuropulmonary blastoma, thyroid goiter, etc. Our case has not undergone genetic testing, but a consult was placed for further workup.