CT
What's the typical distribution of cerebral calcifications in Fahr syndrome?
Symmetrical calcification of basal ganglia and thalamus. Additionally, calcification of subcortical white matter and cerebellar dentate nuclei may be found.
What is the clinical presentation of Fahr syndrome?
Clinical presentation is variable. Many patients are asymptomatic while others may suffer from cognitive impairment to dementia, gait disturbance, basal ganglia movement disorders or sensory changes.
What's the difference between Fahr disease and Fahr syndrome?
Fahr disease, also known as primary familial brain calcification, is a congenital disorder while Fahr syndrome has a secondary cause.
Symmetric calcified deposits in basal ganglia, cerebellum and subcortical white matter. No other anomalies.