The patient underwent a right VATS pleurodesis and right upper lobe wedge resection.
Pathology demonstrated:
MICROSCOPIC DESCRIPTION:
Sections of lung show randomly dispersed areas of interstitial smooth muscle proliferation composed of bland spindle cells. Several cystically dilated air-spaces contain a similar smooth muscle proliferation within the cyst wall. A subpleural bulla is also present. There is no evidence of atypia or malignancy. Immunohistochemical results show spindle cells stain: SMA+, HMB45-, MelanA- and Synaptophysin-. The histological features are those of lymphangioleiomyomatosis. Clinical and radiological correlation is recommended.
DIAGNOSIS:
Right lung, upper lobe, wedge resection: Lymphangioleiomyomatosis.