CT - Lung and soft tissue windows
What are the four main findings that characterize Scimitar syndrome?
1) Hypoplastic lung (almost exclusively right lung) 2) An anomalous pulmonary vein draining into the systemic venous system (IVC is the most common) 3) Cardiac dextroposition 4) Right pulmonary artery hypoplasia
Besides the IVC, what are two other sites that the anomalous vein can drain into?
Right atrium and portal vein
When viewing the frontal chest radiograph, what are some differential diagnoses that one should consider?
Lobar atelectasis Unilateral absence of pulmonary artery Pulmonary vein varix Pulmonary sequestration Congenital pulmonary venolobar syndrome Meandering pulmonary vein
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two anomalous pulmonary veins located in the right lung that both drain into the IVC
main scimitar vein is located anteriorly and superiorly relative to the second anomalous vein
the smaller vein is partly calcified
cardiac dextroposition and right lung hypoplasia
hyparterial right main bronchus with abnormal branching pattern
bronchial wall thickening and mild bronchiectasis in the right lung
left pulmonary artery asymmetrically larger than the right (best seen in the coronal plane)
focal consolidation in the left upper lobe, consistent with pneumonia