Photo
The first photo illustrates the right hand which shows large linear epidermal nevi on the dorsum of the hand. It also shows asymmetric enlargement of the thumb, index and middle fingers (macrodystrophia lipomatosis). A small connective tissue nevus is just adjacent to the thumb.
The second image demonstrates the left hand which shows asymmetric enlargement of the index and middle fingers.
The third image shows the palmar aspects of both hands with characteristic connective tissue nevi on the palmar thenar aspect of the right hand.
The fourth image shows the most important and specific feature of Proteus syndrome which is the cerebriform connective tissue nevus on the plantar aspect of the right foot.
The fifth image demonstrates the left foot smaller cerebriform connective tissue nevi and little toe bluish discoloration (likely venous vascular malformation).