The Barkovich classification of interhemispheric cysts associated with agenesis of corpus callosum (ACC) includes type 1 cysts, which appear unilocular and communicate with lateral or third ventricles (diverticula), and type 2 cysts, which are often multiloculated and do not appear to communicate with the ventricular system ¹.

Type 2 cysts are further divided on the basis of imaging appearance and co-existing morphology. Type 2c cysts are associated with subcortical heterotopia and thus the diagnosis in this instance ¹.

Additionally, in the presence of asymmetric ventriculomegaly and dysgenesis of the corpus callosum along with the interhemispheric cyst, features are suggesting the triad of congenital cerebral anomalies: Asymmetric ventriculomegaly, interhemispheric cyst and dysgenesis of the corpus callosum (AVID).