Sturge-Weber syndrome, or encephalotrigeminal angiomatosis, is a phacomatosis characterized by facial port wine stains and pial angiomas.
CT findings:
- detects subcortical calcification at an earlier age than plain film and can also demonstrate associated parenchymal volume loss
-
tram-track sign of cortical and subcortical calcification 1,2
- calvarial and regional sinus enlargement may be evident
- ipsilateral choroid plexus may be enlarged
- in severe cases, a Dyke-Davidoff-Masson appearance may be seen
- orbital choroidal hemangiomas may be present
- asymmetric cavernous sinus enlargement 3