Congenital urethrovaginal fistula is an extremely rare entity which is part of the urogenital sinus abnormalities. As such, it is known to be associated with other genitourinary malformations including renal agenesis, uterine agenesis and cloaca malformations.

Usual presentation is poor urinary stream and dribbling of urine. Urinary tract infection and pain may be other presentations. Few case have presented as late as 25 years of age.

Micturating cysto urethrography reveals the fistulous communication and the contrast filled vagina is seen as a oblong pouch posterior to the urinary bladder and urethra. MRI of abdomen and pelvis should accompany MCU to exclude other urogenital malformations.