Atretic parietal cephalocele

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Atretic parietal cephalocele (APC) also known as atertic cephalocele, refers to small subscalp lesion which consists of dura, fibrous tissue, and dysplastic brain tissue.

Epidemiology

Common presentation in infants and young children. 

Clinical presentation

Palpable midline parietal soft tissue mass.

Pathology

It is thought to represent involuted true cephalocele (meningocele or encephalocele) connected to dura matter via a fibrous stalk.

Associations

Increased incidence of intracranial anomalies.

Radiographic features

  • subgaleal soft  tissue mass with intracranial extension via sharply demarcated calvarial defect (cranium bifidum)
  • CSF tract and vertical falcine vein point to the subcutaneous scalp mass
  • vertically oriented primitive falcine vein
  • fibrous stalk connecting the cephalocele
  • focal fenestration of superior sagittal sinus at the atretic parietal cephalocele
  • prominence of superior cerebellar cistern and suprapineal recess
  • superior peaking of the posterior tentorium
  • spinning top configuration of the tentorial incisura

Differential diagnosis

Imaging differential considerations include

Prognosis

PrognosisThe prognosis of atertic cephalocels isatretic cephalocoeles are generally good.

See also

  • -<p><strong>Atretic parietal c</strong><strong>ephalocele</strong> (<strong>APC</strong>) also known as <strong>atertic <a href="/articles/cephalocoele">cephalocele</a></strong>, refers to small subscalp lesion which consists of dura, fibrous tissue, and dysplastic brain tissue.</p><h4>Epidemiology</h4><p>Common presentation in infants and young children. </p><h4>Clinical presentation</h4><p>Palpable midline parietal soft tissue mass.</p><h4>Pathology</h4><p>It is thought to represent involuted true cephalocele (<a title="Meningocele" href="/articles/meningocoele">meningocele</a> or <a title="Encephalocele" href="/articles/encephalocoele">encephalocele</a>) connected to dura matter via a fibrous stalk.<strong> </strong></p><h5>Associations</h5><p>Increased incidence of intracranial anomalies.</p><h4>Radiographic features</h4><ul>
  • +<p><strong>Atretic parietal c</strong><strong>ephalocele</strong> (<strong>APC</strong>) also known as <strong>atertic <a href="/articles/cephalocoele">cephalocele</a></strong>, refers to small subscalp lesion which consists of dura, fibrous tissue, and dysplastic brain tissue.</p><h4>Epidemiology</h4><p>Common presentation in infants and young children. </p><h4>Clinical presentation</h4><p>Palpable midline parietal soft tissue mass.</p><h4>Pathology</h4><p>It is thought to represent involuted true cephalocele (<a href="/articles/meningocoele">meningocele</a> or <a href="/articles/encephalocoele">encephalocele</a>) connected to dura matter via a fibrous stalk.<strong> </strong></p><h5>Associations</h5><p>Increased incidence of intracranial anomalies.</p><h4>Radiographic features</h4><ul>
  • -</ul><h4>Differential diagnosis</h4><ul>
  • -<li>sinus pericranii</li>
  • +</ul><h4>Differential diagnosis</h4><p>Imaging differential considerations include</p><ul>
  • +<li><a title="Sinus pericranii" href="/articles/sinus-pericranii">sinus pericranii</a></li>
  • -<li>cephalohematoma</li>
  • +<li><a title="Cephalohaematoma" href="/articles/cephalohaematoma">cephalohaematoma</a></li>
  • -<li>vascular lesions (hemangioma)</li>
  • -</ul><h4>Prognosis</h4><p>Prognosis of atertic cephalocels is generally good.</p><h4>See also</h4><p><a href="/articles/cephalocoele">Cephalocoele</a></p>
  • +<li>vascular lesions (haemangioma)</li>
  • +</ul><h4>Prognosis</h4><p>The prognosis of atretic cephalocoeles are generally good.</p><h4>See also</h4><ul><li><a href="/articles/cephalocoele">cephalocoele</a></li></ul>

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