Congenital renal anomalies comprise of vast spectrum of pathologies and include:
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congenital cystic renal disease
infantile polycystic renal disease: autosomal recessive polycystic kidney disease (ARPKD): Potter type I
multicystic dysplastic kidneys: Potter type II
early onset autosomal dominant polycystic kidney disease (ADPKD): Potter type III
obstructive cystic renal dysplasia: Potter type IV
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obstructive renal disease
congenital PUJ obstruction
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pretumorous conditions
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renal morphological anomalies / renal fusional anomalies
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congenital renal positional anomalies
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tumours presenting in antenatal: childhood period
Associated syndromes
Meckel Gruber syndrome: dominant feature
MURCS association: dominant feature
VACTERL association: dominant feature