Citation, DOI, disclosures and article data
Citation:
Weerakkody Y, Ayesa S, Desmoplastic small round cell tumour of the pleura. Reference article, Radiopaedia.org (Accessed on 26 Mar 2025) https://doi.org/10.53347/rID-99418
Desmoplastic small round cell tumour (DSRCT) of the pleura is a rare primary pleural malignancy comprising of mesenchymal cells.
Epidemiology
Tend to occur in younger patients (mean ~ 25.5 years) and with a slightly greater male predilection.
Treatment and prognosis
DSRCT tend to be aggressive tumours with a poor prognosis.
History and etymology
DSRCT was first described in 1989 by Gerald and Rosai and Ordonez et al. as a highly aggressive and rare mesenchymal tumour arising from serosal surfaces.
See also
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1. Fois A, Pirina P, Arcadu A et al. Desmoplastic Small Round Cell Tumors of the Pleura: A Review of the Clinical Literature. Multidiscip Respir Med. 2017;12(1):22. doi:10.1186/s40248-017-0103-6 - Pubmed
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2. Parkash V, Gerald W, Parma A, Miettinen M, Rosai J. Desmoplastic Small Round Cell Tumor of the Pleura. Am J Surg Pathol. 1995;19(6):659-65. doi:10.1097/00000478-199506000-00006 - Pubmed
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3. Cao Y, Chen Y, Yang L et al. Desmoplastic Small Round Cell Tumor: A Case Report of a Rare Differential Diagnosis of Solid Tumors of the Pleura. Oncol Lett. 2015;10(5):2991-5. doi:10.3892/ol.2015.3680 - Pubmed
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