Congenital scoliosis - wedge, semisegmented, and segmented hemivertebrae

Case contributed by Leonardo Lustosa
Diagnosis certain

Presentation

Scoliotic spine since birth. No other known congenital anomalies.

Patient Data

Age: 4 years
Gender: Female
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Info

Congenital scoliosis with a right lumbar and a left thoracolumbar curves.

Wedge vertebra (hypoplastic left half of the vertebral body).

Semisegmented hemivertebra.

(Fully) segmented hemivertebra.

Even shoulders. No pelvic obliquity. No coronal imbalance.

Case Discussion

Congenital osteogenic scoliosis, often called congenital scoliosis, refers to the scoliosis resulting from vertebral malformations.

In this case, three types of vertebral malformations are present:

  • wedge vertebra: half of the vertebral body is underdeveloped

  • semisegmented hemivertebra: vertebra lacking formation of half of its body and fused with the vertebra above or below

  • (fully) segmented hemivertebra: vertebra lacking formation of half of its body and not attached to the vertebra above or below

Both wedge vertebrae and segmented hemivertebrae have the potential to progress to severe curves. In the present case, these are on opposite sites of their correspondent convexities, which partially compensate for the curves, resulting in scoliosis without uneven shoulders.

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