Haemangioblastoma

Case contributed by A.Prof Frank Gaillard

Presentation

Polycythaemia for investigation.

Patient Data

Age: 60 years
CT

In the posterior fossa, abutting the inferior surface of the tentorium is a large vividly enhancing mass with a central region of cystic change. 

MRI

MRI confirms the presence of a vividly enhancing mass located peripherally in the left cerebellar hemisphere abutting the tentorium. There is surrounding high T2 signal consistent with oedema. Best seen on T2 are prominent flow voids. 

Features are almost certainly those of a hemangioblastoma. 

DSA (angiography)

The tumour in the left superior cerebellar hemisphere near the vermis, is markedly hypervascular, with a rapid arteriovenous shunting very large veins at the dorsal and superior surface of the tumour. There are numerous arterial enlarged feeding arteries, predominantly from the left superior cerebellar artery, but with contribution from a small posterior cerebral artery branch, and left posterior inferior cerebellar artery, and to lesser extent anterior inferior cerebellar artery. A 5-French guiding catheter was placed in the left vertebral artery, and a SL team microcatheter navigated in to the left superior cerebellar artery, well beyond the brainstem, with selective, and embolisation with PTA particles 150-250 micron. No neurologic complications, the procedure was tolerated well, there is good devascularisation of the tumour. Groin closure with six French AngioSeal device.

Conclusion: Marked decrease in tumour blush post pre operative embolisation of haemangioblastoma

Case Discussion

The patient went on to have surgery.

Histology

MICROSCOPIC DESCRIPTION: The sections show scattered stromal cells in a background of many capillary-sized blood vessels. Some of the vessels contain foreign body material, consistent with preoperative embolisation. The tumour cells have mildly enlarged nuclei with hyperchromasia and foamy vacuolated cytoplasm. Mitoses are inconspicuous. There is no necrosis. The features are those of haemangioblastoma. There is no evidence of malignancy.

FINAL DIAGNOSIS: Haemangioblastoma (WHO Grade I)

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Case information

rID: 45138
Case created: 16th May 2016
Last edited: 19th May 2016
Inclusion in quiz mode: Included

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