Presentation
Chest pain
Patient Data
Age: 45 years
Gender: Male
From the case:
Unilateral pulmonary artery atresia
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Info
The right pulmonary artery is absent. Dilated pulmonary trunk and left main pulmonary artery. The right lung is hypoplastic.
Case Discussion
Unilateral pulmonary artery atresia (UPAA) is a congenital defect believed to result from the embryonic sixth aortic arch failing to connect with the pulmonary trunk during development. Although commonly identified in pediatric patients with cardiac anomalies, it can sometimes be diagnosed in adults, either incidentally or more frequently during an evaluation for hemoptysis.
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