This patient presents with features of Sturge-Weber syndrome with new onset of seizures. She had a background history of unilateral left glaucoma, retinal detachment and multiple ophthalmological surgical interventions which failed to save her vision. She has a left-sided facial port wine stain, and a contralateral right-sided choroidal hemangioma confirmed on dedicated ophthalmologic and MRI assessment.

There are unusual infratentorial, ipsilateral, left cerebellar, cortical and subcortical calcifications. Cerebellar pial angiomatosis has been documented in rare cases of Sturge-Weber syndrome.

In view of the heterogeneous salivary gland appearance, the possibility of fungal sinusitis and the presence of lymph adenopathy, immune suppression and connective tissue disorders were offered as differentials.

Non-contrast CT brain/sinuses and gadolinium administration were contraindicated due to her recent pregnant status (3 months gestation at the time of presentation and imaging).