Congenital ossicular anomalies

A.Prof Frank Gaillard et al.

Congenital anomalies of the ossicles are most frequently associated with external ear abnormalities also, although they can occur in isolation. 

They cause conductive hearing loss (CHL).

When bilateral they are most frequently genetic, with autosomal dominant inheritance, whereas unilateral anomalies are usually sporadic.

Isolated ossicular anomalies can be classified as

  • class I : stapedial ankylosis
  • class II : stapedial ankylosis with other associated anomalies
  • class III : ossicular anomalies withouth stapedial ankylosis
  • class IV : oval / round dysplasia

They are associated with numerous syndromes including

Share article

Article information

rID: 1166
Synonyms or Alternate Spellings:

Support Radiopaedia and see fewer ads

Cases and figures

  • Drag
    Ossicles Annotated
    Drag here to reorder.
  • Updating… Please wait.

    Alert accept

    Error Unable to process the form. Check for errors and try again.

    Alert accept Thank you for updating your details.