Streak ovaries are a form of ovarian dysgenesis and are most commonly associated with Turner syndrome, but can also be seen in other disorders of gender development 3. Occasionally they may be functional and secondary sexual characteristics may develop.
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Epidemiology
Associations
Turner syndrome: 45,XO karyotype 3
triple X syndrome (trisomy X): 47,XXX karyotype 2
"pure" gonadal dysgenesis: 46,XX karyotype 3
46,XY (male) karyotype with varying degrees of failure of masculinization, termed "complete" gonadal dysgenesis in its most severe form 3
Pathology
Failure of normal gonadal development, resulting in underdeveloped or undifferentiated gonadal tissue 4.
Radiographic features
Imaging will demonstrate unilateral or bilateral streak-like structures in place of the ovary, or along the course of the round ligament 1. Accompanying Müllerian duct anomalies may be identified at the same time.
Ultrasound
streak ovaries may contain no or very few ovarian follicles
can be difficult to identify due to small size
MRI
more sensitive than ultrasound 3