Eisenmenger syndrome in transposition of the great arteries with cor uniloculare biatriatum
Diagnosis certain
Presentation
Known congenital heart defect, Dyspnea, cyanosis, hemoptysis. CT performed to rule out pulmonary embolism.
Patient Data
Age: 25 years
Gender: Male
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Transposition of the great arteries (TGA). Dilatation of the pulmonary arteries with abrupt change in diameter due to pulmonary hypertension. Rudimentary ventricular septum (functional cor uniloculare biatriatum). Delicate thoracic aorta.