Presentation
Recurrent lower abdominal pain. Initial ultrasound noted a pelvic cystic lesion.
Patient Data
Age: 15 years
Gender: Female
From the case:
Herlyn-Werner-Wunderlich syndrome
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Info
Uterine didelphys and the left Mullerian duct derivatives are distended with fluid consistent with blood signal intensity. There is ipsilateral kidney agenesis and the contralateral kidney is hypertrophied with normal-appearing contralateral Mullerian duct derivatives.
Case Discussion
Herlyn-Werner-Wunderlich syndrome encompasses
- uterine didelphys with vaginal septum causing hemivaginal obstruction
- consequent unilateral hematocolpos, hematometra, hemosalpix and occasionally hemoperitoneum
- contralateral Mullerian duct is well developed so that the patient presentation is often vague as there is no amenorrhea.
- ipsilateral renal agenesis with compensatory hypertrophy of the contralateral kidney
This patient underwent resection of the left hemiuterus with improvement of her symptoms.
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