Acute pulmonary oedema, mitral regurgitation and mucopolysaccharidosis

Case contributed by Dr Craig Hacking

Presentation

Post emergency intubation. Clinically has APO.

Patient Data

Age: 30 years
Gender: Female

The ETT and NGT are well-positioned. Tubing through the right side of the neck and over the midline of the chest likely represents VP shunt tubing which is intact.

The heart is enlarged even allowing for projection, and there is abnormal cardiac contour, in keeping with history of mitral valve disease.

There is diffuse air space opacification, more so on the right side, with perihilar infiltrates. No pleural effusion or evidence of pneumothorax. Features are in keeping with asymmetric acute pulmonary oedema.

Posterior ribs are abnormal, in keeping with history of MPS.

Case Discussion

Three diagnoses on the one CXR! The patient has a background history of mitral regurgitation and is known to have MPS VI (Maroteaux-Lamy syndrome).

Mitral regurg is a known cause of unilateral APO.

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Case information

rID: 56239
Case created: 20th Oct 2017
Last edited: 2nd Nov 2017
System: Chest
Inclusion in quiz mode: Included

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