Ebstein anomaly

Case contributed by Dr Vincent Tatco


History of progressive exertional dyspnea and episodes of cyanosis. Physical examination revealed a murmur. Electrocardiography demonstrated right bundle-branch block.

Patient Data

Age: 10
Gender: Female
Modality: X-ray

There is marked cardiomegaly with a huge right atrial margin and somewhat squared or box-shaped appearance. 

The aorta and main pulmonary artery segment are not well delineated. 

The visualized pulmonary vascularity is within normal to slightly decreased.  


Modality: Annotated image

Annotated image showing the box-shaped heart.

Author: Vincent Tatco

License: CC-NC-BY-SA

Case Discussion

This case shows the radiographic appearance of the cardiac silhouette in an echocardiographically proven Ebstein anomaly.

PlayAdd to Share

Case Information

rID: 43277
Case created: 3rd Mar 2016
Last edited: 3rd Dec 2016
Inclusion in quiz mode: Included

Updating… Please wait.

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.