Fahr disease

Case contributed by Dr David Cuete

Patient Data

Age: 55
Gender: Female
CT

CT brain

Unenhanced CT show shows bilateral calcifications, slightly asymmetrical in the basal ganglia and the thalamus, also the dentate nucleus are calcified.

Case Discussion

Bilateral striopallidodentate calcinosis (BSPDC), commonly known as Fahr disease, is a rare syndrome characterised by symmetrical calcification of the basal ganglion and dentate nucleus. The basal ganglia are the most common site of involvement. Most cases present with extrapyramidal symptoms initially.

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Case information

rID: 22843
Case created: 28th Apr 2013
Last edited: 24th Sep 2015
Inclusion in quiz mode: Included

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