Fahr disease

Case contributed by David Cuete
Diagnosis almost certain

Patient Data

Age: 55 years
Gender: Female

CT brain

ct

Unenhanced CT show shows bilateral calcifications, slightly asymmetrical in the basal ganglia and the thalamus, also the dentate nucleus are calcified.

Case Discussion

Bilateral striopallidodentate calcinosis (BSPDC), commonly known as Fahr disease, is a rare syndrome characterized by symmetrical calcification of the basal ganglion and dentate nucleus. The basal ganglia are the most common site of involvement. Most cases present with extrapyramidal symptoms initially.

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