Presentation
Patient presented with lymphangioma circumscriptum in right upper limb extending into chest wall. Additional features include hypertrophy of phalanges.
Patient Data

Overgrowth of 1st-3rd metacarpals and phalanges in right hand and soft tissue overgrowth in the left forearm and hand.




Multiple hyperechoic lesions throughout the spleen, probably hemangiomas.



There are multiple hyperintense masses throughout the spleen, perhaps hemangiomas. Heterogeneous, predominately hyperintense lesions along the right chest wall, consistent with a vascular malformation.
Case Discussion
The combination of skeletal, soft tissue and vascular findings is consistent with a congenital overgrowth syndrome associated with vascular anomalies, probably Klippel-Trénaunay syndrome.